# | Title | Journal | Year | Citations |
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1 | Hepatocytes corrected by gene therapy are selected in vivo in a murine model of hereditary tyrosinaemia type I | Nature Genetics | 1996 | 546 |
2 | Intracellular processing of endothelial nitric oxide synthase isoforms associated with differences in severity of cardiopulmonary diseases: Cleavage of proteins with aspartate vs. glutamate at position 298 | Proceedings of the National Academy of Sciences of the United States of America | 2000 | 497 |
3 | MMP1 and MMP7 as Potential Peripheral Blood Biomarkers in Idiopathic Pulmonary Fibrosis | PLoS Medicine | 2008 | 467 |
4 | Molecules in the ARF Orbit | Journal of Biological Chemistry | 1998 | 323 |
5 | Progressive Preclinical Interstitial Lung Disease in Rheumatoid Arthritis | Archives of Internal Medicine | 2008 | 319 |
6 | Comprehensive Evaluation of 35 Patients With Lymphangioleiomyomatosis | Chest | 1999 | 301 |
7 | Structure and Function of ARF Proteins: Activators of Cholera Toxin and Critical Components of Intracellular Vesicular Transport Processes | Journal of Biological Chemistry | 1995 | 299 |
8 | Prevalence and Clinical Characteristics of Lymphangioleiomyomatosis (LAM) in Patients with Tuberous Sclerosis Complex | American Journal of Respiratory and Critical Care Medicine | 2001 | 290 |
9 | Cytokine-mediated Transcriptional Induction of the Human Inducible Nitric Oxide Synthase Gene Requires Both Activator Protein 1 and Nuclear Factor κB-binding Sites | Journal of Biological Chemistry | 1998 | 281 |
10 | Identification and Characterization of a Mammalian 39-kDa Poly(ADP-ribose) Glycohydrolase | Journal of Biological Chemistry | 2006 | 242 |
11 | Decline in Lung Function in Patients With Lymphangioleiomyomatosis Treated With or Without Progesterone | Chest | 2004 | 217 |
12 | β-Arrestin-mediated ADP-ribosylation Factor 6 Activation and β2-Adrenergic Receptor Endocytosis | Journal of Biological Chemistry | 2001 | 204 |
13 | Cyclic nucleotide phosphodiesterase 3A–deficient mice as a model of female infertility | Journal of Clinical Investigation | 2004 | 203 |
14 | Release of full-length 55-kDa TNF receptor 1 in exosome-like vesicles: A mechanism for generation of soluble cytokine receptors | Proceedings of the National Academy of Sciences of the United States of America | 2004 | 196 |
15 | Effect of pirfenidone on the pulmonary fibrosis of Hermansky–Pudlak syndrome | Molecular Genetics and Metabolism | 2002 | 185 |
16 | Regulation and function of the cyclic nucleotide phosphodiesterase (PDE3) gene family | Progress in Molecular Biology and Translational Science | 2000 | 176 |
17 | Pulmonary Function and High-Resolution CT Findings in Patients With an Inherited Form of Pulmonary Fibrosis, Hermansky-Pudlak Syndrome, Due to Mutations in HPS-1 | Chest | 2000 | 169 |
18 | Shedding of the Type II IL-1 Decoy Receptor Requires a Multifunctional Aminopeptidase, Aminopeptidase Regulator of TNF Receptor Type 1 Shedding | Journal of Immunology | 2003 | 169 |
19 | Early Interstitial Lung Disease in Familial Pulmonary Fibrosis | American Journal of Respiratory and Critical Care Medicine | 2007 | 157 |
20 | Analysis of the Cytokine-Stimulated Human Inducible Nitric Oxide Synthase (iNOS) Gene: Characterization of Differences between Human and Mouse iNOS Promoters | Biochemical and Biophysical Research Communications | 1998 | 152 |
21 | Cytohesin-1, a cytosolic guanine nucleotide-exchange protein for ADP-ribosylation factor | Proceedings of the National Academy of Sciences of the United States of America | 1997 | 150 |
22 | Mitogen-activated Protein Kinases Mediate Activator Protein-1-dependent Human Inducible Nitric-oxide Synthase Promoter Activation | Journal of Biological Chemistry | 2001 | 150 |
23 | Purification and Cloning of a Brefeldin A-inhibited Guanine Nucleotide-exchange Protein for ADP-ribosylation Factors | Journal of Biological Chemistry | 1999 | 145 |
24 | Mechanisms of Soluble Cytokine Receptor Generation | Journal of Immunology | 2004 | 144 |
25 | Helicobacter pylori Vacuolating Cytotoxin Induces Activation of the Proapoptotic Proteins Bax and Bak, Leading to Cytochrome c Release and Cell Death, Independent of Vacuolation | Journal of Biological Chemistry | 2006 | 132 |
26 | An Aminopeptidase, ARTS-1, Is Required for Interleukin-6 Receptor Shedding | Journal of Biological Chemistry | 2003 | 128 |
27 | Lymphangioleiomyomatosis | Cancer Control | 2006 | 125 |
28 | Identification of ARTS-1 as a novel TNFR1-binding protein that promotes TNFR1 ectodomain shedding | Journal of Clinical Investigation | 2002 | 123 |
29 | ADP ribosylation of human neutrophil peptide-1 regulates its biological properties | Proceedings of the National Academy of Sciences of the United States of America | 2002 | 117 |
30 | ARF-GEP100, a guanine nucleotide-exchange protein for ADP-ribosylation factor 6 | Proceedings of the National Academy of Sciences of the United States of America | 2001 | 107 |
31 | Cloning and expression of a cDNA encoding a bovine brain brefeldin A-sensitive guanine nucleotide-exchange protein for ADP-ribosylation factor | Proceedings of the National Academy of Sciences of the United States of America | 1997 | 103 |
32 | The 39-kDa poly(ADP-ribose) glycohydrolase ARH3 hydrolyzes O-acetyl-ADP-ribose, a product of the Sir2 family of acetyl-histone deacetylases | Proceedings of the National Academy of Sciences of the United States of America | 2006 | 103 |
33 | Alternative Splicing of Human Inducible Nitric-Oxide Synthase mRNA | Journal of Biological Chemistry | 1996 | 99 |
34 | Isoforms of Cyclic Nucleotide Phosphodiesterase PDE3 and Their Contribution to cAMP Hydrolytic Activity in Subcellular Fractions of Human Myocardium | Journal of Biological Chemistry | 2005 | 99 |
35 | Glyceraldehyde-3-phosphate Dehydrogenase Enhances Transcriptional Activity of Androgen Receptor in Prostate Cancer Cells | Journal of Biological Chemistry | 2007 | 97 |
36 | Brefeldin A-inhibited guanine nucleotide-exchange activity of Sec7 domain from yeast Sec7 with yeast and mammalian ADP ribosylation factors | Proceedings of the National Academy of Sciences of the United States of America | 1998 | 96 |
37 | Role of phosphodiesterase type 3A and 3B in regulating platelet and cardiac function using subtype-selective knockout mice | Cellular Signalling | 2007 | 91 |
38 | Down-regulation of cyclic-nucleotide phosphodiesterase 3B in 3T3-L1 adipocytes induced by tumour necrosis factor α and cAMP | Biochemical Journal | 2000 | 90 |
39 | Maximal Oxygen Uptake and Severity of Disease in Lymphangioleiomyomatosis | American Journal of Respiratory and Critical Care Medicine | 2003 | 89 |
40 | Similarities in Function and Gene Structure of Cytohesin-4 and Cytohesin-1, Guanine Nucleotide-exchange Proteins for ADP-ribosylation Factors | Journal of Biological Chemistry | 2000 | 88 |
41 | Different ARF Domains Are Required for the Activation of Cholera Toxin and Phospholipase D | Journal of Biological Chemistry | 1995 | 84 |
42 | Erdheim-Chester Disease: A Rare Multisystem Histiocytic Disorder Associated with Interstitial Lung Disease | American Journal of the Medical Sciences | 2001 | 84 |
43 | Helicobacter pylori-mediated transcriptional regulation of the human beta-defensin 2 gene requires NF-kappaB | Cellular Microbiology | 2001 | 84 |
44 | ARL4D Recruits Cytohesin-2/ARNO to Modulate Actin Remodeling | Molecular Biology of the Cell | 2007 | 84 |
45 | Helicobacter pylori VacA Activates the p38/Activating Transcription Factor 2-mediated Signal Pathway in AZ-521 Cells | Journal of Biological Chemistry | 2004 | 83 |
46 | Characterization of an ADP-ribosylation Factor-like 1 Protein inSaccharomyces cerevisiae | Journal of Biological Chemistry | 1997 | 82 |
47 | Stimulation of Signal Transducer and Activator of Transcription-1 (STAT1)-dependent Gene Transcription by Lipopolysaccharide and Interferon-γ Is Regulated by Mammalian Target of Rapamycin | Journal of Biological Chemistry | 2003 | 80 |
48 | Cloning and characterization of human inducible nitric oxide synthase splice variants: A domain, encoded by exons 8 and 9, is critical for dimerization | Proceedings of the National Academy of Sciences of the United States of America | 1998 | 77 |
49 | Extracellular TNFR1 Release Requires the Calcium-dependent Formation of a Nucleobindin 2-ARTS-1 Complex | Journal of Biological Chemistry | 2006 | 77 |
50 | Pulmonary Artery Pressure in Lymphangioleiomyomatosis | Chest | 2007 | 77 |