| # | Title | Journal | Year | Citations |
|---|
| 1 | Guidelines for the use and interpretation of assays for monitoring autophagy (4th edition)1 | Autophagy | 2021 | 1,430 |
| 2 | Clinical diagnosis of progressive supranuclear palsy: The movement disorder society criteria | Movement Disorders | 2017 | 1,402 |
| 3 | High levels of mitochondrial DNA deletions in substantia nigra neurons in aging and Parkinson disease | Nature Genetics | 2006 | 1,363 |
| 4 | Near infrared spectroscopy (NIRS): A new tool to study hemodynamic changes during activation of brain function in human adults | Neuroscience Letters | 1993 | 1,055 |
| 5 | Heparin treatment in sinus venous thrombosis | Lancet, The | 1991 | 956 |
| 6 | CADASIL | Lancet Neurology, The | 2009 | 939 |
| 7 | Real-time imaging reveals the single steps of brain metastasis formation | Nature Medicine | 2010 | 935 |
| 8 | Mutation in the neuronal voltage-gated sodium channel SCN1A in familial hemiplegic migraine | Lancet, The | 2005 | 760 |
| 9 | Differential effects on motorcortical inhibition induced by blockade of GABA uptake in humans | Journal of Physiology | 1999 | 758 |
| 10 | Progressive degeneration of nigrostriatal dopamine neurons following intrastriatal terminal lesions with 6-hydroxydopamine: A combined retrograde tracing and immunocytochemical study in the rat | Neuroscience | 1994 | 718 |
| 11 | Treatment and outcomes of acute basilar artery occlusion in the Basilar Artery International Cooperation Study (BASICS): a prospective registry study | Lancet Neurology, The | 2009 | 640 |
| 12 | The phenotypic spectrum of CADASIL: Clinical findings in 102 cases | Annals of Neurology | 1998 | 618 |
| 13 | EFNS guidelines on the diagnosis and management of European Lyme neuroborreliosis | European Journal of Neurology | 2010 | 585 |
| 14 | Mutations in the gene encoding ɛ-sarcoglycan cause myoclonus–dystonia syndrome | Nature Genetics | 2001 | 523 |
| 15 | Vestibular loss causes hippocampal atrophy and impaired spatial memory in humans | Brain | 2005 | 518 |
| 16 | Nesprin-1 and -2 are involved in the pathogenesis of Emery–Dreifuss muscular dystrophy and are critical for nuclear envelope integrity | Human Molecular Genetics | 2007 | 461 |
| 17 | A randomized placebo-controlled trial of idebenone in Leber’s hereditary optic neuropathy | Brain | 2011 | 461 |
| 18 | BAFF is produced by astrocytes and up-regulated in multiple sclerosis lesions and primary central nervous system lymphoma | Journal of Experimental Medicine | 2005 | 441 |
| 19 | Pneumococcal meningitis in adults: Spectrum of complications and prognostic factors in a series of 87 cases | Brain | 2003 | 432 |
| 20 | Episodic vertigo related to migraine (90 cases): vestibular migraine? | Journal of Neurology | 1999 | 409 |
| 21 | Reciprocal inhibitory visual-vestibular interaction. Visual motion stimulation deactivates the parieto-insular vestibular cortex | Brain | 1998 | 403 |
| 22 | Methylprednisolone, Valacyclovir, or the Combination for Vestibular Neuritis | New England Journal of Medicine | 2004 | 403 |
| 23 | Mutations in dynamin 2 cause dominant centronuclear myopathy | Nature Genetics | 2005 | 390 |
| 24 | Vestibular cortex lesions affect the perception of verticality | Annals of Neurology | 1994 | 386 |
| 25 | Reduced striatal dopamine transporters in idiopathic rapid eye movement sleep behaviour disorder | Brain | 2000 | 386 |
| 26 | Spatial patterns of neuroimaging biomarker change in individuals from families with autosomal dominant Alzheimer's disease: a longitudinal study | Lancet Neurology, The | 2018 | 383 |
| 27 | Multisensory Cortical Signal Increases and Decreases During Vestibular Galvanic Stimulation (fMRI) | Journal of Neurophysiology | 2001 | 379 |
| 28 | C-terminal truncations in human 3′-5′ DNA exonuclease TREX1 cause autosomal dominant retinal vasculopathy with cerebral leukodystrophy | Nature Genetics | 2007 | 366 |
| 29 | Ocular torsion and tilt of subjective visual vertical are sensitive brainstem signs | Annals of Neurology | 2004 | 357 |
| 30 | Brain activation patterns during imagined stance and locomotion in functional magnetic resonance imaging | NeuroImage | 2004 | 340 |
| 31 | Cerebral generators involved in the pathogenesis of the restless legs syndrome | Annals of Neurology | 1997 | 338 |
| 32 | Vestibular syndromes in the roll plane: Topographic diagnosis from brainstem to cortex | Annals of Neurology | 1994 | 336 |
| 33 | A placebo-controlled trial of insulin-like growth factor-I in amyotrophic lateral sclerosis | Neurology | 1998 | 333 |
| 34 | European Academy of Neurology guideline on the diagnosis of coma and other disorders of consciousness | European Journal of Neurology | 2020 | 331 |
| 35 | Biotechnological agents for the immunotherapy of multiple sclerosis. Principles, problems and perspectives | Brain | 1997 | 330 |
| 36 | Gene–environment interactions in Leber hereditary optic neuropathy | Brain | 2009 | 307 |
| 37 | Targeted next generation sequencing as a diagnostic tool in epileptic disorders | Epilepsia | 2012 | 299 |
| 38 | Anti-LRP4 autoantibodies in AChR- and MuSK-antibody-negative myasthenia gravis | Journal of Neurology | 2012 | 297 |
| 39 | Pathophysiology of Bacterial Meningitis: Mechanism(s) of Neuronal Injury | Journal of Infectious Diseases | 2002 | 290 |
| 40 | Phobic Postural Vertigo | Neurology | 1996 | 282 |
| 41 | Pallidal neurostimulation in patients with medication-refractory cervical dystonia: a randomised, sham-controlled trial | Lancet Neurology, The | 2014 | 281 |
| 42 | Transplantation of Genetically Corrected Human iPSC-Derived Progenitors in Mice with Limb-Girdle Muscular Dystrophy | Science Translational Medicine | 2012 | 269 |
| 43 | Wallenberg's syndrome: Lateropulsion, cyclorotation, and subjective visual vertical in thirty-six patients | Annals of Neurology | 1992 | 267 |
| 44 | The role of EEG in epilepsy: A critical review | Epilepsy and Behavior | 2009 | 263 |
| 45 | Neuron-glia communication via EphA4/ephrin-A3 modulates LTP through glial glutamate transport | Nature Neuroscience | 2009 | 258 |
| 46 | L-Dopa Therapy of Uremic and Idiopathic Restless Legs Syndrome: A Double-Blind, Crossover Trial | Sleep | 1995 | 257 |
| 47 | Latent Herpesvirus Infection in Human Trigeminal Ganglia Causes Chronic Immune Response | American Journal of Pathology | 2003 | 257 |
| 48 | Long-term prognosis and causes of death in CADASIL: a retrospective study in 411 patients | Brain | 2004 | 253 |
| 49 | Risk variants for atrial fibrillation on chromosome 4q25 associate with ischemic stroke | Annals of Neurology | 2008 | 253 |
| 50 | Early increase of CSF sTREM2 in Alzheimer’s disease is associated with tau related-neurodegeneration but not with amyloid-β pathology | Molecular Neurodegeneration | 2019 | 253 |
