| # | Title | Journal | Year | Citations |
|---|
| 1 | Movement Disorder Society‐sponsored revision of the Unified Parkinson's Disease Rating Scale (MDS‐UPDRS): Scale presentation and clinimetric testing results | Movement Disorders | 2008 | 4,796 |
| 2 | Movement Disorder Society-sponsored revision of the Unified Parkinson's Disease Rating Scale (MDS-UPDRS): Process, format, and clinimetric testing plan | Movement Disorders | 2007 | 1,097 |
| 3 | Guideline of transthyretin-related hereditary amyloidosis for clinicians | Orphanet Journal of Rare Diseases | 2013 | 525 |
| 4 | Targeting Chelatable Iron as a Therapeutic Modality in Parkinson's Disease | Antioxidants and Redox Signaling | 2014 | 488 |
| 5 | Treatment of paraneoplastic neurological syndromes with antineuronal antibodies (Anti-Hu, Anti-Yo) with a combination of immunoglobulins, cyclophosphamide, and methylprednisolone | Journal of Neurology, Neurosurgery and Psychiatry | 2000 | 356 |
| 6 | Genome-wide association study identifies 19p13.3 (UNC13A) and 9p21.2 as susceptibility loci for sporadic amyotrophic lateral sclerosis | Nature Genetics | 2009 | 344 |
| 7 | Pure alexia as a disconnection syndrome: New diffusion imaging evidence for an old concept | Cortex | 2008 | 271 |
| 8 | Alzheimer's disease associated with mutations in presenilin 2 is rare and variably penetrant | Human Molecular Genetics | 1996 | 259 |
| 9 | Anti-HMGCR Autoantibodies in European Patients With Autoimmune Necrotizing Myopathies | Medicine (United States) | 2014 | 235 |
| 10 | Limbic encephalitis and small cell lung cancer. Clinical and immunological features | Brain | 1997 | 230 |
| 11 | A Path Toward Precision Medicine for Neuroinflammatory Mechanisms in Alzheimer's Disease | Frontiers in Immunology | 2020 | 201 |
| 12 | The role of dominant premotor cortex in language: a study using intraoperative functional mapping in awake patients | NeuroImage | 2003 | 196 |
| 13 | Immunosuppressive therapy is more effective than interferon in neuromyelitis optica | Multiple Sclerosis Journal | 2007 | 190 |
| 14 | Phase 1 trial of a CpG oligodeoxynucleotide for patients with recurrent glioblastoma1 | Neuro-Oncology | 2006 | 189 |
| 15 | A prospective study of cognitive functions following conventional radiotherapy for supratentorial gliomas in young adults: 4-year results | International Journal of Radiation Oncology Biology Physics | 1996 | 171 |
| 16 | Intravenous immunoglobulin treatment in paraneoplastic neurological syndromes with antineuronal autoantibodies. | Journal of Neurology, Neurosurgery and Psychiatry | 1996 | 170 |
| 17 | Peripheral neuropathy associated with IgM monoclonal gammopathy: Correlations between M-protein antibody activity and clinical/electrophysiological features in 40 cases | | 1998 | 164 |
| 18 | Riluzole in Huntington's disease: a 3‐year, randomized controlled study | Annals of Neurology | 2007 | 160 |
| 19 | Dystonia rating scales: Critique and recommendations | Movement Disorders | 2013 | 150 |
| 20 | Memory complaints in young and elderly subjects | International Journal of Geriatric Psychiatry | 1999 | 149 |
| 21 | Radiographic findings in 37 cases of primary CNS lymphoma in immunocompetent patients | European Radiology | 2002 | 144 |
| 22 | Productive and perceptive language reorganization in temporal lobe epilepsy | NeuroImage | 2005 | 137 |
| 23 | Prevalence of amyloid‐β pathology in distinct variants of primary progressive aphasia | Annals of Neurology | 2018 | 132 |
| 24 | EEG evidence of compensatory mechanisms in preclinical Alzheimer’s disease | Brain | 2019 | 131 |
| 25 | Parkinson's disease dementia: Definitions, guidelines, and research perspectives in diagnosis | Annals of Neurology | 2008 | 122 |
| 26 | Clinical profile of patients with ATP1A3 mutations in Alternating Hemiplegia of Childhood—a study of 155 patients | Orphanet Journal of Rare Diseases | 2015 | 117 |
| 27 | Autoimmune disorders and quadrivalent human papillomavirus vaccination of young female subjects | Journal of Internal Medicine | 2014 | 116 |
| 28 | Evaluation of treatment response in adults with relapsing MOG-Ab-associated disease | Journal of Neuroinflammation | 2019 | 115 |
| 29 | Descriptive epidemiology of cerebral gliomas in France | Cancer | 1997 | 114 |
| 30 | Early Cognitive, Structural, and Microstructural Changes in Presymptomatic C9orf72 Carriers Younger Than 40 Years | JAMA Neurology | 2018 | 108 |
| 31 | Cerebral Edema Associated with Meningiomas: Possible Role of a Secretory-Excretory Phenomenon | Neurosurgery | 1984 | 101 |
| 32 | Peripheral neuropathy associated with essential mixed cryoglobulinaemia: a role for hepatitis C virus infection? | Journal of Neurology, Neurosurgery and Psychiatry | 1996 | 101 |
| 33 | Guidelines for the preclinical in vivo evaluation of pharmacological active drugs for ALS/MND: Report on the 142nd ENMC international workshop | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2007 | 98 |
| 34 | Health-related quality of life in patients with high-risk low-grade glioma (EORTC 22033-26033): a randomised, open-label, phase 3 intergroup study | Lancet Oncology, The | 2016 | 97 |
| 35 | Neurologic manifestations associated with COVID-19: a multicentre registry | Clinical Microbiology and Infection | 2021 | 95 |
| 36 | Krabbe disease in adults: phenotypic and genotypic update from a series of 11 cases and a review | Journal of Inherited Metabolic Disease | 2013 | 94 |
| 37 | How to apply the movement disorder society criteria for diagnosis of progressive supranuclear palsy | Movement Disorders | 2019 | 93 |
| 38 | A ferroptosis–based panel of prognostic biomarkers for Amyotrophic Lateral Sclerosis | Scientific Reports | 2019 | 91 |
| 39 | Cerebral Edema Associated with Meningiomas: Possible Role of a Secretory-Excretory Phenomenon | Neurosurgery | 1984 | 90 |
| 40 | Changing outcome in inflammatory neuropathies | Neurology | 2014 | 89 |
| 41 | Effectiveness of mycophenolate mofetil as first-line therapy in AQP4-IgG, MOG-IgG, and seronegative neuromyelitis optica spectrum disorders | Multiple Sclerosis Journal | 2017 | 89 |
| 42 | Multiple infusions of anti-epidermal growth factor receptor (EGFR) monoclonal antibody (EMD 55 900) in patients with recurrent malignant gliomas | European Journal of Cancer | 1996 | 87 |
| 43 | Intra-operative mapping of the subcortical visual pathways using direct electrical stimulations | Acta Neurochirurgica | 2004 | 86 |
| 44 | European Federation of Neurological Societies/Peripheral Nerve Society guideline on management of multifocal motor neuropathy* | European Journal of Neurology | 2006 | 86 |
| 45 | Apathy and the basal ganglia | Journal of Neurology | 2006 | 85 |
| 46 | Primary writing tremor and writer's cramp: Two faces of a same coin? | Movement Disorders | 2013 | 84 |
| 47 | Linking neuroscience with modern concepts of impulse control disorders in Parkinson's disease | Movement Disorders | 2015 | 84 |
| 48 | Intravenous immunoglobulin as short- and long-term therapy of multifocal motor neuropathy: a retrospective study of response to IVIg and of its predictive criteria in 40 patients | Journal of Neurology, Neurosurgery and Psychiatry | 2008 | 83 |
| 49 | The COMT Val158Met polymorphism affects the response to entacapone in Parkinson's disease: A randomized crossover clinical trial | Annals of Neurology | 2011 | 82 |
| 50 | Directional leads for deep brain stimulation: Opportunities and challenges | Movement Disorders | 2017 | 81 |
