# | Title | Journal | Year | Citations |
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1 | Prognostic factors in ALS: A critical review | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2009 | 839 |
2 | Consensus criteria for the diagnosis of frontotemporal cognitive and behavioural syndromes in amyotrophic lateral sclerosis | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2009 | 475 |
3 | A brain-computer interface for long-term independent home use | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2010 | 443 |
4 | Design, power, and interpretation of studies in the standard murine model of ALS | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2008 | 435 |
5 | Guidelines for preclinical animal research in ALS/MND: A consensus meeting | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2010 | 293 |
6 | Investigation of the therapeutic effects of edaravone, a free radical scavenger, on amyotrophic lateral sclerosis (Phase II study) | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2006 | 216 |
7 | Awaji diagnostic algorithm increases sensitivity of El Escorial criteria for ALS diagnosis | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2009 | 196 |
8 | Beyond Guam: The cyanobacteria/BMAA hypothesis of the cause of ALS and other neurodegenerative diseases | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2009 | 170 |
9 | Good practice in the management of amyotrophic lateral sclerosis: Clinical guidelines. An evidence‐based review with good practice points. EALSC Working Group | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2007 | 168 |
10 | Detecting frontotemporal dysfunction in ALS: Utility of the ALS Cognitive Behavioral Screen (ALS-CBS™) | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2010 | 167 |
11 | How common are behavioural changes in amyotrophic lateral sclerosis? | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2011 | 165 |
12 | Global brain atrophy and corticospinal tract alterations in ALS, as investigated by voxel‐based morphometry of 3‐D MRI | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2005 | 160 |
13 | What would brain-computer interface users want? Opinions and priorities of potential users with amyotrophic lateral sclerosis | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2011 | 157 |
14 | Cyanobacteria and BMAA exposure from desert dust: A possible link to sporadic ALS among Gulf War veterans | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2009 | 145 |
15 | ALS in Italian professional soccer players: The risk is still present and could be soccer-specific | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2009 | 144 |
16 | Oxidative stress biomarkers in sporadic ALS | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2008 | 141 |
17 | Causes of death in a post‐mortem series of ALS patients | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2008 | 140 |
18 | The sex ratio in amyotrophic lateral sclerosis: A population based study | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2010 | 140 |
19 | Impaired glucose tolerance in patients with amyotrophic lateral sclerosis | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2010 | 139 |
20 | Nationwide survey of juvenile muscular atrophy of distal upper extremity (Hirayama disease) in Japan | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2006 | 137 |
21 | High metabolic level in patients with familial amyotrophic lateral sclerosis | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2009 | 135 |
22 | Phase 2 study of sodium phenylbutyrate in ALS | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2009 | 135 |
23 | Early use of non‐invasive ventilation prolongs survival in subjects with ALS | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2007 | 131 |
24 | A cluster of amyotrophic lateral sclerosis in New Hampshire: A possible role for toxic cyanobacteria blooms | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2009 | 130 |
25 | Detecting neurobehavioral changes in amyotrophic lateral sclerosis | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2007 | 129 |
26 | ALSOD: The Amyotrophic Lateral Sclerosis Online Database | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2008 | 128 |
27 | Treatment with lithium carbonate does not improve disease progression in two different strains of SOD1 mutant mice | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2009 | 127 |
28 | The syndromes of frontotemporal dysfunction in amyotrophic lateral sclerosis | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2008 | 126 |
29 | Dysarthria in amyotrophic lateral sclerosis: A review | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2010 | 126 |
30 | Electrical impedance myography as a biomarker to assess ALS progression | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2012 | 125 |
31 | Exposure to chemicals and metals and risk of amyotrophic lateral sclerosis: A systematic review | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2009 | 124 |
32 | Amyotrophic lateral sclerosis and frontotemporal dementia: A behavioural and cognitive continuum | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2012 | 124 |
33 | Does interneuronal dysfunction contribute to neurodegeneration in amyotrophic lateral sclerosis? | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2012 | 121 |
34 | Proposed criteria for familial amyotrophic lateral sclerosis | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2011 | 120 |
35 | A systematic review of behavioural changes in motor neuron disease | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2012 | 118 |
36 | The cognitive profile of amyotrophic lateral sclerosis: A meta-analysis | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2010 | 116 |
37 | A phase II trial of talampanel in subjects with amyotrophic lateral sclerosis | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2010 | 114 |
38 | A decrease in body mass index is associated with faster progression of motor symptoms and shorter survival in ALS | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2010 | 114 |
39 | Amyotrophic lateral sclerosis, physical exercise, trauma and sports: Results of a population-based pilot case-control study | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2010 | 110 |
40 | Biochemical alterations associated with ALS | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2012 | 108 |
41 | Excellent inter‐rater, intra‐rater, and telephone‐administered reliability of the ALSFRS‐R in a multicenter clinical trial | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2007 | 107 |
42 | The epidemiology and treatment of ALS: Focus on the heterogeneity of the disease and critical appraisal of therapeutic trials | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2011 | 107 |
43 | Autonomic dysfunction in ALS: A preliminary study on the effects of intrathecal BDNF | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2005 | 102 |
44 | A randomized, placebo-controlled trial of memantine for functional disability in amyotrophic lateral sclerosis | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2010 | 101 |
45 | Effect of genetic background on phenotype variability in transgenic mouse models of amyotrophic lateral sclerosis: A window of opportunity in the search for genetic modifiers | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2011 | 101 |
46 | Guidelines for the preclinical in vivo evaluation of pharmacological active drugs for ALS/MND: Report on the 142nd ENMC international workshop | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2007 | 98 |
47 | Timelines in the diagnostic evaluation of people with suspected amyotrophic lateral sclerosis (ALS)/motor neuron disease (MND) – a 20-year review: Can we do better? | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2010 | 94 |
48 | Analysis of factors that modify susceptibility and rate of progression in amyotrophic lateral sclerosis (ALS) | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2006 | 92 |
49 | Creatine monohydrate in ALS: Effects on strength, fatigue, respiratory status and ALSFRS | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2008 | 92 |
50 | Combined riluzole and sodium phenylbutyrate therapy in transgenic amyotrophic lateral sclerosis mice | Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders | 2009 | 91 |