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exaly
›
Journals
›
Journal of Cystic Fibrosis
›
top-articles
Journal of Cystic Fibrosis
0.8
(top 50%)
impact factor
14.0K
(top 1%)
papers
69.6K
(top 5%)
citations
96
(top 5%)
h
-index
0.9
(top 50%)
extended IF
14.3K
all documents
73.9K
doc citations
150
(top 5%)
g
-index
Top Articles
#
Title
Journal
Year
Citations
1
Evaluation of a new definition for chronic Pseudomonas aeruginosa infection in cystic fibrosis patients
Journal of Cystic Fibrosis
2003
573
2
ECFS best practice guidelines: the 2018 revision
Journal of Cystic Fibrosis
2018
521
3
Consensus on the use and interpretation of cystic fibrosis mutation analysis in clinical practice
Journal of Cystic Fibrosis
2008
493
4
European Cystic Fibrosis Society Standards of Care: Best Practice guidelines
Journal of Cystic Fibrosis
2014
438
5
Treatment of lung infection in patients with cystic fibrosis: Current and future strategies
Journal of Cystic Fibrosis
2012
421
6
High treatment burden in adults with cystic fibrosis: Challenges to disease self-management
Journal of Cystic Fibrosis
2009
399
7
Nutrition in patients with cystic fibrosis: a European Consensus
Journal of Cystic Fibrosis
2002
374
8
Inflammation in cystic fibrosis lung disease: Pathogenesis and therapy
Journal of Cystic Fibrosis
2015
371
9
Ivacaftor potentiation of multiple CFTR channels with gating mutations
Journal of Cystic Fibrosis
2012
367
10
Standards of care for patients with cystic fibrosis: a European consensus
Journal of Cystic Fibrosis
2005
363
11
Chronic Mycobacterium abscessus infection and lung function decline in cystic fibrosis
Journal of Cystic Fibrosis
2010
344
12
Recommendations for the classification of diseases as CFTR-related disorders
Journal of Cystic Fibrosis
2011
339
13
Efficacy and safety of ivacaftor in patients with cystic fibrosis and a non-G551D gating mutation
Journal of Cystic Fibrosis
2014
334
14
Best practice guidance for the diagnosis and management of cystic fibrosis-associated liver disease
Journal of Cystic Fibrosis
2011
332
15
The prevalence of cystic fibrosis in the European Union
Journal of Cystic Fibrosis
2008
325
16
Induction of cathelicidin in normal and CF bronchial epithelial cells by 1,25-dihydroxyvitamin D3
Journal of Cystic Fibrosis
2007
304
17
Pseudomonas aeruginosa lasR mutants are associated with cystic fibrosis lung disease progression
Journal of Cystic Fibrosis
2009
296
18
Effect of ivacaftor on CFTR forms with missense mutations associated with defects in protein processing or function
Journal of Cystic Fibrosis
2014
289
19
Safety, efficacy and convenience of tobramycin inhalation powder in cystic fibrosis patients: The EAGER trial
Journal of Cystic Fibrosis
2011
284
20
Disease modifying genes in cystic fibrosis
Journal of Cystic Fibrosis
2005
283
21
Early intervention and prevention of lung disease in cystic fibrosis: a European consensus
Journal of Cystic Fibrosis
2004
265
22
Eradication of early Pseudomonas aeruginosa infection
Journal of Cystic Fibrosis
2005
263
23
Inhaled medication and inhalation devices for lung disease in patients with cystic fibrosis: A European consensus
Journal of Cystic Fibrosis
2009
223
24
A multi-method assessment of treatment adherence for children with cystic fibrosis
Journal of Cystic Fibrosis
2006
219
25
The role of respiratory viruses in cystic fibrosis
Journal of Cystic Fibrosis
2008
219
26
Prevalence and antimicrobial susceptibility of microorganisms isolated from sputa of patients with cystic fibrosis
Journal of Cystic Fibrosis
2008
217
27
CFTR modulator theratyping: Current status, gaps and future directions
Journal of Cystic Fibrosis
2019
208
28
Guidelines for the management of pregnancy in women with cystic fibrosis
Journal of Cystic Fibrosis
2008
205
29
A survey of newborn screening for cystic fibrosis in Europe
Journal of Cystic Fibrosis
2007
204
30
Ultrastructural characterization of cystic fibrosis sputum using atomic force and scanning electron microscopy
Journal of Cystic Fibrosis
2012
199
31
Early aggressive eradication therapy for intermittent Pseudomonas aeruginosa airway colonization in cystic fibrosis patients: 15 years experience
Journal of Cystic Fibrosis
2008
197
32
European best practice guidelines for cystic fibrosis neonatal screening
Journal of Cystic Fibrosis
2009
196
33
Review: Staphylococcus aureus and MRSA in cystic fibrosis
Journal of Cystic Fibrosis
2011
193
34
Innate immunity in cystic fibrosis lung disease
Journal of Cystic Fibrosis
2012
191
35
Longitudinal association between medication adherence and lung health in people with cystic fibrosis
Journal of Cystic Fibrosis
2011
186
36
General introduction to section C: Biochemistry and Biophysics of CFTR
Journal of Cystic Fibrosis
2004
185
37
Mouse models of cystic fibrosis: Phenotypic analysis and research applications
Journal of Cystic Fibrosis
2011
185
38
Disease progression in patients with cystic fibrosis treated with ivacaftor: Data from national US and UK registries
Journal of Cystic Fibrosis
2020
185
39
Emerging bacterial pathogens and changing concepts of bacterial pathogenesis in cystic fibrosis
Journal of Cystic Fibrosis
2015
170
40
Pulmonary exacerbation: Towards a definition for use in clinical trials. Report from the EuroCareCF Working Group on outcome parameters in clinical trials
Journal of Cystic Fibrosis
2011
165
41
Up-to-date and projected estimates of survival for people with cystic fibrosis using baseline characteristics: A longitudinal study using UK patient registry data
Journal of Cystic Fibrosis
2018
165
42
The relative frequency of CFTR mutation classes in European patients with cystic fibrosis
Journal of Cystic Fibrosis
2014
164
43
Lung clearance index: Evidence for use in clinical trials in cystic fibrosis
Journal of Cystic Fibrosis
2014
164
44
Airway glucose concentrations and effect on growth of respiratory pathogens in cystic fibrosis
Journal of Cystic Fibrosis
2007
163
45
Update on cystic fibrosis-related diabetes
Journal of Cystic Fibrosis
2013
160
46
Lung transplant referral for individuals with cystic fibrosis: Cystic Fibrosis Foundation consensus guidelines
Journal of Cystic Fibrosis
2019
154
47
European Cystic Fibrosis Society Standards of Care: Framework for the Cystic Fibrosis Centre
Journal of Cystic Fibrosis
2014
153
48
Guidelines for the diagnosis and management of distal intestinal obstruction syndrome in cystic fibrosis patients
Journal of Cystic Fibrosis
2011
151
49
Established cell lines used in cystic fibrosis research
Journal of Cystic Fibrosis
2004
149
50
European cystic fibrosis bone mineralisation guidelines
Journal of Cystic Fibrosis
2011
147
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