0.8(top 50%)
impact factor
14.0K(top 1%)
papers
69.6K(top 5%)
citations
96(top 5%)
h-index
0.9(top 50%)
extended IF
14.3K
all documents
73.9K
doc citations
150(top 5%)
g-index

Top Articles

#TitleJournalYearCitations
1Evaluation of a new definition for chronic Pseudomonas aeruginosa infection in cystic fibrosis patientsJournal of Cystic Fibrosis2003573
2ECFS best practice guidelines: the 2018 revisionJournal of Cystic Fibrosis2018521
3Consensus on the use and interpretation of cystic fibrosis mutation analysis in clinical practiceJournal of Cystic Fibrosis2008493
4European Cystic Fibrosis Society Standards of Care: Best Practice guidelinesJournal of Cystic Fibrosis2014438
5Treatment of lung infection in patients with cystic fibrosis: Current and future strategiesJournal of Cystic Fibrosis2012421
6High treatment burden in adults with cystic fibrosis: Challenges to disease self-managementJournal of Cystic Fibrosis2009399
7Nutrition in patients with cystic fibrosis: a European ConsensusJournal of Cystic Fibrosis2002374
8Inflammation in cystic fibrosis lung disease: Pathogenesis and therapyJournal of Cystic Fibrosis2015371
9Ivacaftor potentiation of multiple CFTR channels with gating mutationsJournal of Cystic Fibrosis2012367
10Standards of care for patients with cystic fibrosis: a European consensusJournal of Cystic Fibrosis2005363
11Chronic Mycobacterium abscessus infection and lung function decline in cystic fibrosisJournal of Cystic Fibrosis2010344
12Recommendations for the classification of diseases as CFTR-related disordersJournal of Cystic Fibrosis2011339
13Efficacy and safety of ivacaftor in patients with cystic fibrosis and a non-G551D gating mutationJournal of Cystic Fibrosis2014334
14Best practice guidance for the diagnosis and management of cystic fibrosis-associated liver diseaseJournal of Cystic Fibrosis2011332
15The prevalence of cystic fibrosis in the European UnionJournal of Cystic Fibrosis2008325
16Induction of cathelicidin in normal and CF bronchial epithelial cells by 1,25-dihydroxyvitamin D3Journal of Cystic Fibrosis2007304
17Pseudomonas aeruginosa lasR mutants are associated with cystic fibrosis lung disease progressionJournal of Cystic Fibrosis2009296
18Effect of ivacaftor on CFTR forms with missense mutations associated with defects in protein processing or functionJournal of Cystic Fibrosis2014289
19Safety, efficacy and convenience of tobramycin inhalation powder in cystic fibrosis patients: The EAGER trialJournal of Cystic Fibrosis2011284
20Disease modifying genes in cystic fibrosisJournal of Cystic Fibrosis2005283
21Early intervention and prevention of lung disease in cystic fibrosis: a European consensusJournal of Cystic Fibrosis2004265
22Eradication of early Pseudomonas aeruginosa infectionJournal of Cystic Fibrosis2005263
23Inhaled medication and inhalation devices for lung disease in patients with cystic fibrosis: A European consensusJournal of Cystic Fibrosis2009223
24A multi-method assessment of treatment adherence for children with cystic fibrosisJournal of Cystic Fibrosis2006219
25The role of respiratory viruses in cystic fibrosisJournal of Cystic Fibrosis2008219
26Prevalence and antimicrobial susceptibility of microorganisms isolated from sputa of patients with cystic fibrosisJournal of Cystic Fibrosis2008217
27CFTR modulator theratyping: Current status, gaps and future directionsJournal of Cystic Fibrosis2019208
28Guidelines for the management of pregnancy in women with cystic fibrosisJournal of Cystic Fibrosis2008205
29A survey of newborn screening for cystic fibrosis in EuropeJournal of Cystic Fibrosis2007204
30Ultrastructural characterization of cystic fibrosis sputum using atomic force and scanning electron microscopyJournal of Cystic Fibrosis2012199
31Early aggressive eradication therapy for intermittent Pseudomonas aeruginosa airway colonization in cystic fibrosis patients: 15 years experienceJournal of Cystic Fibrosis2008197
32European best practice guidelines for cystic fibrosis neonatal screeningJournal of Cystic Fibrosis2009196
33Review: Staphylococcus aureus and MRSA in cystic fibrosisJournal of Cystic Fibrosis2011193
34Innate immunity in cystic fibrosis lung diseaseJournal of Cystic Fibrosis2012191
35Longitudinal association between medication adherence and lung health in people with cystic fibrosisJournal of Cystic Fibrosis2011186
36General introduction to section C: Biochemistry and Biophysics of CFTRJournal of Cystic Fibrosis2004185
37Mouse models of cystic fibrosis: Phenotypic analysis and research applicationsJournal of Cystic Fibrosis2011185
38Disease progression in patients with cystic fibrosis treated with ivacaftor: Data from national US and UK registriesJournal of Cystic Fibrosis2020185
39Emerging bacterial pathogens and changing concepts of bacterial pathogenesis in cystic fibrosisJournal of Cystic Fibrosis2015170
40Pulmonary exacerbation: Towards a definition for use in clinical trials. Report from the EuroCareCF Working Group on outcome parameters in clinical trialsJournal of Cystic Fibrosis2011165
41Up-to-date and projected estimates of survival for people with cystic fibrosis using baseline characteristics: A longitudinal study using UK patient registry dataJournal of Cystic Fibrosis2018165
42The relative frequency of CFTR mutation classes in European patients with cystic fibrosisJournal of Cystic Fibrosis2014164
43Lung clearance index: Evidence for use in clinical trials in cystic fibrosisJournal of Cystic Fibrosis2014164
44Airway glucose concentrations and effect on growth of respiratory pathogens in cystic fibrosisJournal of Cystic Fibrosis2007163
45Update on cystic fibrosis-related diabetesJournal of Cystic Fibrosis2013160
46Lung transplant referral for individuals with cystic fibrosis: Cystic Fibrosis Foundation consensus guidelinesJournal of Cystic Fibrosis2019154
47European Cystic Fibrosis Society Standards of Care: Framework for the Cystic Fibrosis CentreJournal of Cystic Fibrosis2014153
48Guidelines for the diagnosis and management of distal intestinal obstruction syndrome in cystic fibrosis patientsJournal of Cystic Fibrosis2011151
49Established cell lines used in cystic fibrosis researchJournal of Cystic Fibrosis2004149
50European cystic fibrosis bone mineralisation guidelinesJournal of Cystic Fibrosis2011147